{"id":24337,"date":"2020-08-07T17:38:06","date_gmt":"2020-08-07T15:38:06","guid":{"rendered":"https:\/\/zdravovek.eu\/?p=24337"},"modified":"2020-09-11T16:05:21","modified_gmt":"2020-09-11T14:05:21","slug":"systemovy-lupus-erythematodes","status":"publish","type":"post","link":"https:\/\/zdravovek.eu\/cs\/systemovy-lupus-erythematodes\/","title":{"rendered":"Syst\u00e9mov\u00fd lupus erythematodes (SLE) &#8211; co to je, p\u0159\u00edznaky, diagnostika, l\u00e9\u010dba"},"content":{"rendered":"<p><strong>Lupus (syst\u00e9mov\u00fd lupus erythematodes, SLE)<\/strong> pat\u0159\u00ed mezi autoimunitn\u00ed onemocn\u011bn\u00ed. Obecn\u011b jsou autoimunitn\u00ed onemocn\u011bn\u00ed charakteristick\u00e1 zm\u011bnami v imunitn\u00ed odpov\u011bdi, kdy bu\u0148ky <strong>napadaj\u00ed vlastn\u00ed tk\u00e1n\u011b a org\u00e1ny<\/strong> a chovaj\u00ed se k nim jako k patogen\u016fm.<\/p>\n<p>Jak\u00e9 m\u00e1 syst\u00e9mov\u00fd lupus <strong>p\u0159\u00edznaky, jak prob\u00edh\u00e1 diagnostika a l\u00e9\u010dba<\/strong> zjist\u00edte n\u00ed\u017ee:<\/p>\n\n<h2>Co to je lupus?<\/h2>\n<p>Lupus je <strong>z\u00e1va\u017en\u00e9, chronick\u00e9 <a href=\"https:\/\/zdravovek.eu\/autoimunitne-ochorenia-zoznam\/\">autoimunitn\u00ed onemocn\u011bn\u00ed<\/a><\/strong>, kter\u00e9 je charakteristick\u00e9 t\u00edm, \u017ee postihuje mnoh\u00e9 org\u00e1ny t\u011bla. Nej\u010dast\u011bji je posti\u017eena k\u016f\u017ee, ledviny, klouby, krevn\u00ed bu\u0148ky a nervov\u00fd syst\u00e9m. Na nemoc lupus jsou <strong>n\u00e1chyln\u011bj\u0161\u00ed \u017eeny<\/strong>, ve srovn\u00e1n\u00ed s mu\u017ei se u nich vyskytuje a\u017e 10:1. K rozvoji onemocn\u011bn\u00ed doch\u00e1z\u00ed zejm\u00e9na mezi <strong>20. &#8211; 30. rokem \u017eivota<\/strong>.<\/p>\n<p><strong>P\u0159esn\u00fd mechanismus<\/strong>, pro\u010d k nemoci lupus doch\u00e1z\u00ed, <strong>nen\u00ed zn\u00e1m<\/strong>. Dosud je zn\u00e1mo jen to, \u017ee onemocn\u011bn\u00ed p\u0159edch\u00e1z\u00ed po\u0161kozen\u00ed rovnov\u00e1hy imunitn\u00edho syst\u00e9mu. Po\u0161kozen\u00ed se t\u00fdk\u00e1 zejm\u00e9na T- a B-lymfocyt\u016f, makrof\u00e1g\u016f a dendritick\u00fdch bun\u011bk. Na rozvoj onemocn\u011bn\u00ed m\u00e1 vliv i genetika.<\/p>\n<div class=\"erit-block erit-block-interesting\"> <strong>Lupus vulgaris<\/strong> je naopak bakteri\u00e1ln\u00ed, naka\u017eliv\u00e9 tuberkul\u00f3zn\u00ed onemocn\u011bn\u00ed. Bakterie odpov\u011bdn\u00e1 za rozvoj t\u00e9to nemoci je <em><strong>Mycobacterium tuberculosis<\/strong><\/em>. Podobn\u011b jako syst\u00e9mov\u00fd lupus, i p\u0159\u00edznaky lupus vulgaris se nej\u010dast\u011bji vyskytuj\u00ed na obli\u010deji v oblasti l\u00edc\u00ed a nosu. P\u0159i nel\u00e9\u010den\u00ed infekce hroz\u00ed rozvoj bolav\u00fdch v\u0159ed\u016f na tv\u00e1\u0159i. <\/div>\n<h3>P\u0159\u00edznaky lupus erythematodes<\/h3>\n<p><strong>Symptomy onemocn\u011bn\u00ed jsou r\u016fzn\u00e9<\/strong>, mezi typick\u00e1 pat\u0159\u00ed nap\u0159\u00edklad:<\/p>\n<ul>\n<li><strong>Ko\u017en\u00ed vyr\u00e1\u017eka<\/strong> &#8211; objevuje se a\u017e u 40 % pacient\u016f. Ve form\u011b fleku ve tvaru mot\u00fdla se nach\u00e1z\u00ed na tv\u00e1\u0159\u00edch. Typick\u00e1 je v aktivn\u00ed form\u011b onemocn\u011bn\u00ed, p\u0159i remisi (potla\u010den\u00ed p\u0159\u00edznak\u016f) obvykle miz\u00ed nebo zm\u00edr\u0148uje svoji intenzitu. P\u0159\u00edtomn\u00e9 mohou b\u00fdt i drobn\u00e9 krusty.<\/li>\n<li><strong>Vyr\u00e1\u017eka ve tvaru disku<\/strong> se objevuje jinde v oblasti obli\u010deji nebo na poko\u017ece hlavy. Rizikem je vznik jizvy, kter\u00e1 se m\u016f\u017ee vytvo\u0159it po vyl\u00e9\u010den\u00ed vyr\u00e1\u017eky.<\/li>\n<li><strong>Fotosenzitivn\u00ed reakce<\/strong> &#8211; po nadm\u011brn\u00e9m vystaven\u00ed poko\u017eky slune\u010dn\u00edmu z\u00e1\u0159en\u00ed se vyr\u00e1\u017eky a pup\u00ednky objev\u00ed a\u017e u 50 &#8211; 70 % pacient\u016f.<\/li>\n<li>V \u00fastech a na nose se \u010dasto objevuj\u00ed <a href=\"https:\/\/zdravovek.eu\/afty\/\"><strong>afty a ranky<\/strong><\/a>.<\/li>\n<li><strong>Klouby<\/strong> jsou <strong>ztuhl\u00e9, bolestiv\u00e9, zan\u00edcen\u00e9<\/strong>, v m\u00edstech se vyskytuje otok &#8211; a\u017e u 80 % pacient\u016f se syst\u00e9mov\u00fdm lupusem.<\/li>\n<li><strong>Pleuritida<\/strong> (<a href=\"https:\/\/zdravovek.eu\/zapal-pohrudnice-pleuritida\/\">z\u00e1n\u011bt pohrudnice<\/a>) &#8211; bolest po bo\u010dn\u00edch stran\u00e1ch plic, intenzivn\u011bj\u0161\u00ed je p\u0159i n\u00e1maze, ka\u0161li a prudk\u00fdch pohybech.<\/li>\n<li><strong>Probl\u00e9my s ledvinami<\/strong> &#8211; <a href=\"https:\/\/zdravovek.eu\/krv-v-moci\/\">v mo\u010di se m\u016f\u017ee vyskytovat krev<\/a> nebo b\u00edlkoviny, k rozvoji z\u00e1n\u011btu ledvin doch\u00e1z\u00ed a\u017e u 50 % pacient\u016f.<\/li>\n<li>\u010cast\u00e1 je i <strong><a href=\"https:\/\/zdravovek.eu\/chronicka-unava-vycerpanost\/\">\u00fanava<\/a>, zv\u00fd\u0161en\u00e1 teplota<\/strong>.<\/li>\n<li><a href=\"https:\/\/zdravovek.eu\/studene-ruky-a-nohy\/\"><strong>Chladn\u00e9 prsty na rukou a nohou<\/strong><\/a> (<a href=\"https:\/\/zdravovek.eu\/raynaudov-syndrom\/\">Raynaud\u016fv syndrom<\/a>), such\u00e9 o\u010di.<\/li>\n<li><strong>Du\u0161nost, <a href=\"https:\/\/zdravovek.eu\/bolest-na-hrudi\/\">bolesti na hrudi<\/a>, bolesti hlavy<\/strong>.<\/li>\n<li>Probl\u00e9my s pam\u011bt\u00ed, <strong><a href=\"https:\/\/zdravovek.eu\/depresia\/\">deprese<\/a>, poruchy koncentrace, zmatenost<\/strong>.<\/li>\n<\/ul>\n<figure id=\"attachment_20354\" aria-describedby=\"caption-attachment-20354\" style=\"width: 1024px\" class=\"wp-caption alignnone\"><img loading=\"lazy\" class=\"wp-image-20354 size-large\" src=\"https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-1024x948.jpg\" alt=\"Syst\u00e9mov\u00fd lupus erythematodes (SLE) - infografika (p\u0159\u00edznaky, diagnostika a l\u00e9\u010dba)\" width=\"1024\" height=\"948\" srcset=\"https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-1024x948.jpg 1024w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-600x555.jpg 600w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-300x278.jpg 300w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-768x711.jpg 768w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-696x644.jpg 696w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-1068x989.jpg 1068w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba-454x420.jpg 454w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/11\/systemovy-lupus-erythematosus-sle-infografika-priznaky-diagnostika-a-liecba.jpg 1280w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><figcaption id=\"caption-attachment-20354\" class=\"wp-caption-text\">Zdroj: 123rf.com<\/figcaption><\/figure>\n<h2>Diagnostika lupusu<\/h2>\n<p>T\u00edm, \u017ee lupus <strong>postihuje mnoho org\u00e1n\u016f<\/strong> a p\u0159\u00edznaky jsou u ka\u017ed\u00e9ho pacienta individu\u00e1ln\u00ed <strong>se diagnostika lupusu komplikuje<\/strong>. Nez\u0159\u00eddka se st\u00e1v\u00e1, \u017ee k rozvoji prvn\u00edch viditeln\u00fdch p\u0159\u00edznak\u016f doch\u00e1z\u00ed a\u017e po p\u00e1r letech od v\u00fdskytu onemocn\u011bn\u00ed, tak\u017ee pacient ani nev\u00ed, \u017ee m\u00e1 syst\u00e9mov\u00fd lupus.<\/p>\n<p>V krvi pacient\u016f s nemoc\u00ed lupus se nach\u00e1zej\u00ed <strong>specifick\u00e9 protil\u00e1tky<\/strong> (nap\u0159\u00edklad lupus antikoagulans) a <strong>proteiny<\/strong>, kter\u00e9 jsou charakteristick\u00e9 pro toto onemocn\u011bn\u00ed. Krom\u011b toho se stanovuje i <strong>hodnota CRP<\/strong> (z\u00e1n\u011btliv\u00fd parametr), sedimentace \u010derven\u00fdch krvinek (FW), po\u010det krevn\u00edch bun\u011bk a biochemick\u00e9 parametry.<\/p>\n<p>Na vy\u0161et\u0159en\u00ed funkce ledvin se <strong>pou\u017e\u00edv\u00e1 laboratorn\u00ed vy\u0161et\u0159en\u00ed mo\u010di<\/strong>. V n\u011bkter\u00fdch p\u0159\u00edpadech se m\u016f\u017ee ud\u011blat i biopsie konkr\u00e9tn\u00ed tk\u00e1n\u011b.<\/p>\n<p>Diagnostick\u00fdm krit\u00e9riem je i <strong>klinick\u00fd obraz pacienta<\/strong>. Na potvrzen\u00ed diagn\u00f3zy je t\u0159eba spl\u0148ovat alespo\u0148 4 typick\u00e9 p\u0159\u00edznaky lupusu erythematodes.<\/p>\n<h2>L\u00e9\u010dba lupusu<\/h2>\n<p>Lupus je <strong>nevyl\u00e9\u010diteln\u00e1 choroba<\/strong>, ale pom\u011brn\u011b dob\u0159e <strong>dok\u00e1\u017eeme kontrolovat jeho projevy<\/strong>. V z\u00e1vislosti na tom, kter\u00fd syst\u00e9m nebo org\u00e1n je nejv\u00edce posti\u017een, se vol\u00ed i individu\u00e1ln\u00ed l\u00e9\u010dba.<\/p>\n<p>Nej\u010dast\u011bji se pou\u017e\u00edvaj\u00ed n\u00e1sleduj\u00edc\u00ed skupiny l\u00e9k\u016f:<\/p>\n<ul>\n<li><strong>Nesteroidn\u00ed antiflogistika (NSAID)<\/strong> &#8211; ibuprofen, naproxen, diclofenac &#8211; protiz\u00e1n\u011btliv\u00e9 a analgetick\u00e9 \u00fa\u010dinky t\u011bchto l\u00e9k\u016f jsou vhodn\u00e9 p\u0159i p\u0159\u00edznac\u00edch lupusu jako bolesti kloub\u016f, <a href=\"https:\/\/zdravovek.eu\/opuchnute-nohy\/\">otok<\/a>, hore\u010dka. Nesteroidn\u00ed antiflogistika nejsou vhodn\u00e1 u pacient\u016f <a href=\"https:\/\/zdravovek.eu\/zaludocne-vredy\/\">s v\u0159edy na \u017ealudku<\/a>, p\u0159i n\u011bkter\u00fdch onemocn\u011bn\u00edch ledvin a srdce, proto l\u00e9ka\u0159e informujte o v\u0161ech onemocn\u011bn\u00edch, kter\u00e1 se u v\u00e1s vyskytla.<\/li>\n<li><strong>Antimalarika<\/strong> &#8211; l\u00e9ky, kter\u00e9 se u\u017e podle n\u00e1zvu vyu\u017e\u00edvaj\u00ed k l\u00e9\u010db\u011b v na\u0161ich kon\u010din\u00e1ch vz\u00e1cn\u00e9 mal\u00e1rie, lze pou\u017e\u00edt i p\u0159i lupus erythematodes. Antimalarika jsou n\u00e1pomocn\u00e1 zejm\u00e9na p\u0159i ko\u017en\u00edch projevech onemocn\u011bn\u00ed a sni\u017euj\u00ed frekvenci relaps\u016f. L\u00e9\u010divo hydroxychlorochin u n\u011bkter\u00fdch lid\u00ed m\u016f\u017ee vyvolat <a href=\"https:\/\/zdravovek.eu\/bolest-zaludka\/\">probl\u00e9my se \u017ealudkem<\/a>. B\u011bhem l\u00e9\u010dby je d\u016fle\u017eit\u00e9 sledovat stav o\u010d\u00ed, proto\u017ee ve velmi vz\u00e1cn\u00fdch p\u0159\u00edpadech m\u016f\u017ee doj\u00edt k po\u0161kozen\u00ed s\u00edtnice.<\/li>\n<li><strong>Kortikosteroidy<\/strong> (nej\u010dast\u011bji prednison, methylprednisolon) jsou siln\u00e9 protiz\u00e1n\u011btliv\u00e9 l\u00e9ky. N\u00e1stup \u00fa\u010dinku je velmi rychl\u00fd, l\u00e9\u010dba kortikosteroidy by v\u0161ak nem\u011bla b\u00fdt dlouhodob\u00e1, proto\u017ee se projev\u00ed jejich vedlej\u0161\u00ed \u00fa\u010dinky.<\/li>\n<li><strong>Imunosupresiva<\/strong> (azathioprin, metotrex\u00e1t) &#8211; l\u00e9ky potla\u010duj\u00edc\u00ed imunitn\u00ed odpov\u011b\u010f se pou\u017e\u00edvaj\u00ed p\u0159i intenzivn\u00edch form\u00e1ch syst\u00e9mov\u00e9ho lupusu.<\/li>\n<li><strong>Biologick\u00e9 l\u00e9ky<\/strong> (rituximab, belimumab) &#8211; pom\u011brn\u011b nov\u00e1, vysoce efektivn\u00ed skupina l\u00e9k\u016f. Biologick\u00e9 l\u00e9ky jsou pod\u00e1v\u00e1ny intraven\u00f3zn\u011b.<\/li>\n<\/ul>\n<div class=\"erit-block erit-block-interesting\"> <strong>V\u011bd\u011bli jste, \u017ee?<\/strong><\/p>\n<p><strong>Lupus latinsky znamen\u00e1 vlk<\/strong>. Existuje n\u011bkolik vysv\u011btlen\u00ed, pro\u010d se onemocn\u011bn\u00ed pojmenovalo pr\u00e1v\u011b po tomto zv\u00ed\u0159eti. Jednou z mo\u017enost\u00ed je to, \u017ee l\u00e9ka\u0159\u016fm fleky na tv\u00e1\u0159i p\u0159ipom\u00ednaly po\u0161kr\u00e1b\u00e1n\u00ed od vlka. Jin\u00e9 vysv\u011btlen\u00ed: fleky na obli\u010deji jsou obvykle ve tvaru \u0161krabo\u0161ky (francouzsky: masque loup &#8211; doslovn\u00fd p\u0159eklad: maska vlka). <\/div>\n<h2>Shrnut\u00ed<\/h2>\n<p>Lupus je <strong>celo\u017eivotn\u00ed autoimunitn\u00ed nemoc<\/strong>, kter\u00e1 postihuje zejm\u00e9na \u017eeny ve v\u011bku 20. &#8211; 30. let. Onemocn\u011bn\u00ed je charakteristick\u00e9 f\u00e1zemi <strong>vzplanut\u00ed (relaps) a zlep\u0161en\u00ed p\u0159\u00edznak\u016f (remise)<\/strong>. Syst\u00e9mov\u00fd lupus nen\u00ed vyl\u00e9\u010diteln\u00fd, spr\u00e1vnou l\u00e9\u010dbou v\u0161ak dok\u00e1\u017eeme zlep\u0161ovat jeho projevy. Pacient\u016fm s lupusem se doporu\u010duje <strong>vyh\u00fdbat se <a href=\"https:\/\/zdravovek.eu\/najlepsie-opalovacie-kremy\/\">nadm\u011brn\u00e9mu slune\u010dn\u00edmu z\u00e1\u0159en\u00ed<\/a> ale i chladu<\/strong>, <a href=\"https:\/\/zdravovek.eu\/studene-ruky-a-nohy\/\">zejm\u00e9na v oblast\u00ed rukou a nohou<\/a>. D\u016fle\u017eit\u00e1 je i \u017eivotospr\u00e1va, omezen\u00ed alkoholu a kou\u0159en\u00ed a dodr\u017eov\u00e1n\u00ed l\u00e9\u010dby ur\u010den\u00e9 l\u00e9ka\u0159em.<\/p>\n<p>Zdroje:<\/p>\n<ul>\n<li><a href=\"https:\/\/en.wikipedia.org\/wiki\/Lupus_vulgaris\" target=\"_blank\" rel=\"noopener noreferrer\">wikipedia.org<\/a><\/li>\n<li><a href=\"https:\/\/www.mayoclinic.org\/diseases-conditions\/lupus\/diagnosis-treatment\/drc-20365790\" target=\"_blank\" rel=\"noopener noreferrer\">mayoclinic.org<\/a><\/li>\n<li><a href=\"http:\/\/www.klubmotylik.sk\/diagnostika\/\" target=\"_blank\" rel=\"noopener noreferrer\">klubmotylik.sk<\/a><\/li>\n<li><a href=\"http:\/\/www.solen.sk\/pdf\/83865260e33376127e8c39e40dee60ef.pdf\" target=\"_blank\" rel=\"noopener noreferrer\">solen.sk<\/a><\/li>\n<li><a href=\"http:\/\/sazch.sk\/zriedkave-choroby\/zriedkave-choroby\/lupus\/\" target=\"_blank\" rel=\"noopener noreferrer\">sazch.sk<\/a><\/li>\n<\/ul>\n<div class='erit-disclaimer'><span class='erit-disclaimer-icon'><span class='erit-disclaimer-text'>!<\/span><\/span><span class='erit-disclaimer-text'>\u010cl\u00e1nek byl vypracov\u00e1n l\u00e9k\u00e1rn\u00edkem av\u0161ak, slou\u017e\u00ed pouze pro informativn\u00ed \u00fa\u010dely - nenahrazuje l\u00e9ka\u0159sk\u00e9 vy\u0161et\u0159en\u00ed, nebo osobn\u00ed setk\u00e1n\u00ed v l\u00e9k\u00e1rn\u011b.<\/span><\/div>\n<script type='text\/javascript' >\n                jQuery(document).ready(function($) {\n    \n                    let data = {\n                        'action': 'render_widget_action',\n                        'postId': null,\n                        'categoryId': null\n                    };\n    \n                    let ajaxUrlFromPHP = 'https:\/\/zdravovek.eu\/wp-admin\/admin-ajax.php';\n                    jQuery.post(ajaxUrlFromPHP, data, function(response) {\n                        if(response == 0){\n                            \/\/ chyba\n                            jQuery( '#eap_top_w' ).html( '' );\n                            jQuery( '#eap_top_w_wrap' ).hide();\n                        } if(response == -1){\n                            \/\/ nenasli ziadne produkty\n                            jQuery( '#eap_top_w' ).html( '' );\n                            jQuery( '#eap_top_w_wrap' ).hide();\n                        } else {\n                            let desktop = $(window).width() > 960;\n                            if(desktop){\n                                jQuery( '#eap_top_w' ).html( response );\n                                jQuery( '#eap_top_w_wrap' ).fadeIn(1000);\n                            } else {\n                                jQuery( '#eap_top_w_mob_chart' ).html( response );\n                                jQuery( '#eap_top_w_mob' ).fadeIn(1000); 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Obecn\u011b jsou autoimunitn\u00ed onemocn\u011bn\u00ed charakteristick\u00e1 zm\u011bnami v imunitn\u00ed odpov\u011bdi, kdy bu\u0148ky napadaj\u00ed vlastn\u00ed tk\u00e1n\u011b a org\u00e1ny a chovaj\u00ed se k nim jako k patogen\u016fm. Jak\u00e9 m\u00e1 syst\u00e9mov\u00fd lupus p\u0159\u00edznaky, jak prob\u00edh\u00e1 diagnostika a l\u00e9\u010dba zjist\u00edte n\u00ed\u017ee: Co to je lupus? Lupus je z\u00e1va\u017en\u00e9, chronick\u00e9 autoimunitn\u00ed onemocn\u011bn\u00ed, [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":20337,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":[],"categories":[125,79],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v15.8 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Syst\u00e9mov\u00fd lupus erythematodes (SLE) - co to je? 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