{"id":17873,"date":"2019-06-24T07:27:44","date_gmt":"2019-06-24T05:27:44","guid":{"rendered":"https:\/\/zdravovek.eu\/?p=17873"},"modified":"2020-09-14T18:58:33","modified_gmt":"2020-09-14T16:58:33","slug":"cysticka-fibroza","status":"publish","type":"post","link":"https:\/\/zdravovek.eu\/cs\/cysticka-fibroza\/","title":{"rendered":"Cystick\u00e1 fibr\u00f3za (nemoc slan\u00fdch d\u011bt\u00ed) &#8211; projevy, diagnostika, progn\u00f3za"},"content":{"rendered":"<p>Cystick\u00e1 fibr\u00f3za (mukoviscid\u00f3za) je <strong>geneticky vrozen\u00e9 onemocn\u011bn\u00ed<\/strong>. Postihuje zejm\u00e9na pl\u00edce, ale i jin\u00e9 org\u00e1ny. Jedn\u00edm z nejzn\u00e1m\u011bj\u0161\u00edch p\u0159\u00edznak\u016f cystick\u00e9 fibr\u00f3zy je <strong>slan\u00e1 poko\u017eka d\u00edt\u011bte<\/strong>. Proto se n\u011bkdy ozna\u010duje tak\u00e9 jako <strong>nemoc slan\u00fdch d\u011bt\u00ed<\/strong>.<\/p>\n<p>P\u0159e\u010dt\u011bte si, jak cystick\u00e1 fibr\u00f3za vznik\u00e1, jak\u00e9 jsou jej\u00ed nej\u010dast\u011bj\u0161\u00ed projevy a jak\u00e1 je <strong>progn\u00f3za p\u0159i l\u00e9\u010db\u011b t\u00e9to n\u00e1ro\u010dn\u00e9 choroby<\/strong>.<\/p>\n\n<h2>Co to je cystick\u00e1 fibr\u00f3za?<\/h2>\n<p><strong>Cystick\u00e1 fibr\u00f3za<\/strong> je z\u00e1va\u017en\u00e9 <strong>genetick\u00e9 onemocn\u011bn\u00ed<\/strong>. Onemocn\u011bn\u00ed postihuje v\u00edce org\u00e1n\u016f. Nejv\u00edce v\u0161ak trp\u00ed <strong>pl\u00edce<\/strong> &#8211; pacient\u016fm se postupn\u011b zhor\u0161uje schopnost d\u00fdch\u00e1n\u00ed.<\/p>\n<blockquote>\n<p style=\"text-align: right;\"><span style=\"font-size: 12pt;\">Jin\u00e9 n\u00e1zvy: nemoc slan\u00fdch d\u011bt\u00ed, zastaral\u00fd n\u00e1zev je <strong>mukoviscid\u00f3za<\/strong>.<\/span><\/p>\n<\/blockquote>\n<h3>Jak doch\u00e1z\u00ed k cystick\u00e9 fibr\u00f3ze?<\/h3>\n<p>Aby se cystick\u00e1 fibr\u00f3za rozvinula u d\u00edt\u011bte, u obou rodi\u010d\u016f mus\u00ed b\u00fdt <strong>p\u0159\u00edtomen po\u0161kozen\u00fd gen<\/strong>, kter\u00fd podmi\u0148uje <strong>vznik onemocn\u011bn\u00ed<\/strong>. U takov\u00fdch rodi\u010d\u016f se v\u0161ak v\u016fbec nemus\u00ed objevit p\u0159\u00edznaky samotn\u00e9 cystick\u00e9 fibr\u00f3zy. Takov\u00ed lid\u00e9 se ozna\u010duj\u00ed jako <strong>nosi\u010di cystick\u00e9 fibr\u00f3zy<\/strong>.<\/p>\n<h3>Genetika<\/h3>\n<p>Pokud se sejdou <strong>dva nosi\u010di po\u0161kozen\u00e9ho genu<\/strong>, neznamen\u00e1 to automaticky, \u017ee d\u00edt\u011b bude trp\u011bt cystickou fibr\u00f3zou.<\/p>\n<p>\u0160ance na vznik onemocn\u011bn\u00ed u dvou nosi\u010d\u016f jsou:<\/p>\n<ul>\n<li><strong>25 %<\/strong> \u017ee d\u00edt\u011b bude m\u00edt cystickou fibr\u00f3zu<\/li>\n<li><strong>50 %<\/strong> \u017ee d\u00edt\u011b bude nosi\u010d po\u0161kozen\u00e9ho genu, ale nebude trp\u011bt samotn\u00fdm onemocn\u011bn\u00edm<\/li>\n<li><strong>25 %<\/strong> \u0161ance, \u017ee d\u00edt\u011b nebude ani nosi\u010d genu, ani nebude m\u00edt p\u0159\u00edznaky<\/li>\n<\/ul>\n<figure id=\"attachment_17912\" aria-describedby=\"caption-attachment-17912\" style=\"width: 1024px\" class=\"wp-caption alignnone\"><img loading=\"lazy\" class=\"wp-image-17912 size-large\" src=\"https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-1024x1024.jpg\" alt=\"Cystrick\u00e1 fibr\u00f3za, choroba slan\u00fdch det\u00ed\" width=\"1024\" height=\"1024\" srcset=\"https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-1024x1024.jpg 1024w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-300x300.jpg 300w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-100x100.jpg 100w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-600x600.jpg 600w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-150x150.jpg 150w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-768x768.jpg 768w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-696x696.jpg 696w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-1068x1068.jpg 1068w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti-420x420.jpg 420w, https:\/\/zdravovek.eu\/wp-content\/uploads\/2019\/04\/cysticka-fibroza-choroba-slanych-deti.jpg 1280w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><figcaption id=\"caption-attachment-17912\" class=\"wp-caption-text\">Zdroj: 123rf.com<\/figcaption><\/figure>\n<h3>Co zp\u016fsobuje cystick\u00e1 fibr\u00f3za<\/h3>\n<p>P\u0159i onemocn\u011bn\u00ed doch\u00e1z\u00ed k <strong>n\u011bkolika po\u0161kozen\u00edm r\u016fzn\u00fdch org\u00e1n\u016f<\/strong>.<\/p>\n<p>Pro cystickou fibr\u00f3zu je typick\u00e9 po\u0161kozen\u00ed bun\u011bk, kter\u00e9 produkuj\u00ed hlen, pot a tr\u00e1vic\u00ed \u0161\u0165\u00e1vy. U zdrav\u00e9ho \u010dlov\u011bka jsou tyto tekutiny \u0159\u00eddk\u00e9 a lepkav\u00e9. V tomto p\u0159\u00edpad\u011b se v\u0161ak st\u00e1vaj\u00ed hust\u00e9 a lepkav\u00e9. To vede k <strong>ucp\u00e1n\u00ed d\u016fle\u017eit\u00fdch \u010d\u00e1st\u00ed org\u00e1n\u016f<\/strong>, \u010d\u00edm\u017e se n\u00e1sledn\u011b zhor\u0161uje jejich fungov\u00e1n\u00ed.<\/p>\n<h2>Projevy<\/h2>\n<p>P\u0159\u00edznaky cystick\u00e9 fibr\u00f3zy jsou <strong>pom\u011brn\u011b individu\u00e1ln\u00ed<\/strong>.<\/p>\n<p>I u jedn\u00e9 osoby se mohou p\u0159\u00edznaky m\u011bnit v z\u00e1vislosti na f\u00e1zi a intenzit\u011b onemocn\u011bn\u00ed. U n\u011bkter\u00fdch lid\u00ed se dokonce stane, \u017ee se prvn\u00ed p\u0159\u00edznaky cystick\u00e9 fibr\u00f3zy objev\u00ed a\u017e v pubert\u011b nebo u mlad\u00fdch dosp\u011bl\u00fdch.<\/p>\n<h3>P\u0159\u00edznaky<\/h3>\n<p><strong>Cystick\u00e1 fibr\u00f3za je charakterizov\u00e1na t\u011bmito p\u0159\u00edznaky<\/strong>:<\/p>\n<ul>\n<li><strong>vy\u0161\u0161\u00ed hladiny soli v potu<\/strong> (proto choroba slan\u00fdch d\u011bt\u00ed &#8211; poko\u017eka nemocn\u00fdch je slan\u00e1)<\/li>\n<li><strong>po\u0161kozen\u00ed d\u00fdchac\u00edho traktu<\/strong> &#8211; dlouhotrvaj\u00edc\u00ed ka\u0161el s po\u010detn\u00fdm hlenem, s\u00edp\u00e1n\u00ed, lap\u00e1n\u00ed po dechu, t\u011b\u017ek\u00e9 zvl\u00e1d\u00e1n\u00ed fyzick\u00e9 z\u00e1t\u011b\u017ee, <a href=\"https:\/\/zdravovek.eu\/upchaty-nos-domace-recepty\/\">ucpan\u00fd nos<\/a> a probl\u00e9my s pl\u00edcemi<\/li>\n<li><strong>po\u0161kozen\u00ed tr\u00e1vic\u00edho traktu<\/strong> &#8211; mastn\u00e1 stolice s v\u00fdrazn\u00fdm z\u00e1pachem, pomal\u00e9 p\u0159ib\u00edr\u00e1n\u00ed a r\u016fst, blokace st\u0159ev, <a href=\"https:\/\/zdravovek.eu\/zapcha\/\">z\u00e1cpy<\/a><\/li>\n<li>porucha tolerance gluk\u00f3zy a\u017e <strong>cukrovka<\/strong> (diabetes mellitus)<\/li>\n<\/ul>\n<h4>Cystick\u00e1 fibr\u00f3za u dosp\u011bl\u00fdch<\/h4>\n<p>Typick\u00e9 <strong>p\u0159\u00edznaky cystick\u00e9 fibr\u00f3zy u dosp\u011bl\u00fdch<\/strong>:<\/p>\n<ul>\n<li><strong>z\u00e1n\u011bty slinivky<\/strong> (pankreatitida)<\/li>\n<li><strong>neplodnost<\/strong><\/li>\n<li>\u010dast\u00e9 <a href=\"https:\/\/zdravovek.eu\/pneumonia-zapal-pluc\/\" rel=\"noopener\"><strong>z\u00e1paly plic<\/strong> (pneumonie)<\/a><\/li>\n<\/ul>\n<h2>Diagnostika<\/h2>\n<p>Hned po narozen\u00ed se prov\u00e1d\u00ed <strong>ka\u017ed\u00e9mu d\u011b\u0165\u00e1tku diagnostick\u00fd screening<\/strong> na cystickou fibr\u00f3zu. Na vy\u0161et\u0159en\u00ed posta\u010d\u00ed mal\u00e1 <strong>kapka krve<\/strong>, kter\u00e1 se odeb\u00edr\u00e1 z pati\u010dky novorozence. Toto vy\u0161et\u0159en\u00ed je velmi d\u016fle\u017eit\u00e9, proto\u017ee cystick\u00e1 fibr\u00f3za by v tomto v\u011bku je\u0161t\u011b nem\u011bla \u017e\u00e1dn\u00e9 p\u0159\u00edznaky. Napom\u016f\u017ee k tomu, aby se onemocn\u011bn\u00ed <strong>za\u010dalo l\u00e9\u010dit co nejd\u0159\u00edve<\/strong> a zpomal\u00ed se progres onemocn\u011bn\u00ed.<\/p>\n<div class=\"erit-block erit-block-interesting\"> Krom\u011b cystick\u00e9 fibr\u00f3zy se u novorozenc\u016f prov\u00e1d\u00ed diagnostika na onemocn\u011bn\u00ed jako <strong>fenylketonurie, vrozen\u00e1 hypotyre\u00f3za, vrozen\u00e1 adren\u00e1ln\u00ed hyperplazie<\/strong>. <\/div>\n<p>Pokud jsou v\u00fdsledky screeningov\u00e9ho testu pozitivn\u00ed, na p\u0159esn\u011bj\u0161\u00ed diagnostiku se n\u00e1sledn\u011b ud\u011blaj\u00ed <strong>genetick\u00e1 vy\u0161et\u0159en\u00ed<\/strong>.<\/p>\n<p>P\u0159i diagnostice star\u0161\u00edch d\u011bt\u00ed a dosp\u011bl\u00fdch (kte\u0159\u00ed nebyli na cystickou fibr\u00f3zu testov\u00e1n\u00ed v d\u011btstv\u00ed) se tak\u00e9 pou\u017e\u00edvaj\u00ed <strong>genetick\u00e9 testy nebo test na obsah soli v potu<\/strong>. Diagnostika star\u0161\u00edch d\u011bt\u00ed a dosp\u011bl\u00fdch se prov\u00e1d\u00ed tehdy, pokud se \u010dasto vyskytuj\u00ed z\u00e1n\u011bty slinivky a plic, objev\u00ed se nosn\u00ed polypy a podobn\u011b. <span class=\"erit-highlight\">V sou\u010dasnosti je 30 % pacient\u016f s cystickou fibr\u00f3zou diagnostikovan\u00fdch v dosp\u011bl\u00e9m v\u011bku. <\/span>\n<h2>L\u00e9\u010dba cystick\u00e9 fibr\u00f3zy<\/h2>\n<p>Bohu\u017eel, cystick\u00e1 fibr\u00f3za nen\u00ed onemocn\u011bn\u00ed, kter\u00e9 je vyl\u00e9\u010diteln\u00e9. Sou\u010dasn\u00e1 medic\u00edna zat\u00edm dok\u00e1\u017ee <strong>jen zpomalit pr\u016fb\u011bh nemoci a zm\u00edrnit p\u0159\u00edznaky<\/strong>.<\/p>\n<p>P\u0159i l\u00e9\u010db\u011b cystick\u00e9 fibr\u00f3zy mus\u00ed spolupracovat n\u011bkolik l\u00e9ka\u0159\u016f z r\u016fzn\u00fdch obor\u016f. Nejide\u00e1ln\u011bj\u0161\u00ed je proto <strong>vyhledat centrum, kde se na cystickou fibr\u00f3zu specializuj\u00ed<\/strong> (Praha &#8211; Motol, Brno) p\u0159\u00edpadn\u011b se zkontaktovat s pacienty v <a href=\"http:\/\/klubcf.sk\/\" target=\"_blank\" rel=\"noopener noreferrer\">Klubu cystick\u00e9 fibr\u00f3zy<\/a>.<\/p>\n<p>C\u00edlem l\u00e9\u010dby je <strong>p\u0159ed<\/strong><strong>ch\u00e1zet \u010dast\u00fdm infekc\u00edm plic<\/strong>, redukovat nadm\u011brnou tvorbu hlenu, zlep\u0161ovat pr\u016fchodnost st\u0159ev a pacientovi zaji\u0161\u0165ovat dostate\u010dnou v\u00fd\u017eivu.<\/p>\n<h3>L\u00e9ky<\/h3>\n<p>Pro l\u00e9\u010dbu cystick\u00e9 fibr\u00f3zy se pou\u017e\u00edvaj\u00ed:<\/p>\n<ul>\n<li><strong>antibiotika<\/strong> (l\u00e9\u010dba a prevence z\u00e1n\u011btu plic)<\/li>\n<li><strong>protiz\u00e1n\u011btliv\u00e9 l\u00e9ky<\/strong>, kter\u00e9 sni\u017euj\u00ed otok v d\u00fdchac\u00edch cest\u00e1ch<\/li>\n<li>l\u00e9ky <strong>\u0159ed\u00edc\u00ed hust\u00fd hlen<\/strong><\/li>\n<li><strong>inhala\u010dn\u00ed spreje<\/strong>, kter\u00e9 roz\u0161i\u0159uj\u00ed \u010d\u00e1sti d\u00fdchac\u00edho traktu (bronchodilat\u00e1tory)<\/li>\n<li><strong>pankreatick\u00e9 enzymy<\/strong> kter\u00e9 napom\u00e1haj\u00ed tr\u00e1ven\u00ed<\/li>\n<\/ul>\n<h3>Prevence infekc\u00ed<\/h3>\n<p>U pacient\u016f s cystickou fibr\u00f3zou je velmi d\u016fle\u017eit\u00e1 <strong>prevence vzniku infekc\u00ed<\/strong>. Doporu\u010duje se proto zv\u00fd\u0161en\u00e1 hygiena a vyh\u00fdb\u00e1n\u00ed se velk\u00fdm kolektiv\u016fm, hlavn\u011b v ch\u0159ipkov\u00e9m obdob\u00ed. Samoz\u0159ejmost\u00ed by m\u011blo b\u00fdt i <a href=\"https:\/\/zdravovek.eu\/povinne-ockovanie-deti-ockovaci-kalendar\/\"><strong>dostupn\u00e9 o\u010dkov\u00e1n\u00ed proti r\u016fzn\u00fdm onemocn\u011bn\u00edm<\/strong><\/a> (nap\u0159\u00edklad \u017eloutenka) p\u0159\u00edpadn\u011b bakteri\u00e1ln\u00edm kmen\u016fm (<em>Streptococcus pneumoniae<\/em>, <em>Haemophilus influenzae<\/em>) a vir\u016fm (virus ch\u0159ipky).<\/p>\n<h3>Rehabilitace<\/h3>\n<p>Vhodn\u00e9 jsou i <strong>rehabilitace<\/strong>, b\u011bhem nich\u017e se <strong>odstra\u0148uje nadbyte\u010dn\u00fd hlen z d\u00fdchac\u00edho traktu<\/strong>. Sou\u010d\u00e1st\u00ed rehabilitace je i <strong>kondi\u010dn\u00ed cvi\u010den\u00ed<\/strong>. Vyb\u00edr\u00e1no je tak, aby ho pacienti s cystickou fibr\u00f3zou zvl\u00e1dali a pom\u00e1halo jim adaptovat se na z\u00e1t\u011b\u017e. Cvi\u010den\u00edm se zlep\u0161uje kardiorespira\u010dn\u00ed kondice, zm\u00edr\u0148uje se dechov\u00e1 nedostate\u010dnost a pl\u00edce se \u010dist\u00ed od nadbyte\u010dn\u00e9ho hlenu.<\/p>\n<h2>Komplikace<\/h2>\n<p>P\u0159i t\u00e9to nemoci m\u016f\u017ee doj\u00edt k n\u011bkter\u00fdm komplikac\u00edm:<\/p>\n<ul>\n<li><strong>Bronchiekt\u00e1zie<\/strong> &#8211; po\u0161kozen\u00ed st\u011bny pr\u016fdu\u0161ek (bronch\u016f) vlivem z\u00e1n\u011btu nebo infekce<\/li>\n<li><strong>Chronick\u00e9 infekce<\/strong> &#8211; zp\u016fsoben\u00e9 jsou hust\u00fdm hlenem v d\u00fdchac\u00edm traktu a dutin\u00e1ch, ve kter\u00e9m se snadno mno\u017e\u00ed bakterie<\/li>\n<li><strong>Nosn\u00ed polypy<\/strong> &#8211; vznikaj\u00ed n\u00e1sledkem otoku a z\u00e1n\u011btu sliznice nosu<\/li>\n<li><strong>Vyka\u0161l\u00e1v\u00e1n\u00ed krve (hemopt\u00fdza)<\/strong> &#8211; vyskytuje se hlavn\u011b u dosp\u00edvaj\u00edc\u00edch a dosp\u011bl\u00fdch, vznik\u00e1 n\u00e1sledkem po\u0161kozen\u00ed \u010d\u00e1st\u00ed d\u00fdchac\u00edho syst\u00e9mu<\/li>\n<li><strong>Pneumotorax<\/strong> &#8211; situace, kdy doch\u00e1z\u00ed k hromad\u011bn\u00ed vzduchu v oblasti mezi pl\u00edcemi a hrudn\u00ed st\u011bnou<\/li>\n<li><strong>Selh\u00e1n\u00ed d\u00fdchac\u00edho syst\u00e9mu<\/strong> &#8211; postupn\u00e9 po\u0161kozov\u00e1n\u00ed plic v n\u011bkter\u00fdch p\u0159\u00edpadech vede a\u017e k \u00fapln\u00e9mu zastaven\u00ed funkce a k \u00famrt\u00ed<\/li>\n<li><strong>Akutn\u00ed exacerbace<\/strong> &#8211; stav, p\u0159i kter\u00e9m se pacientovi zhor\u0161\u00ed d\u00fdch\u00e1n\u00ed, lap\u00e1 po dechu, ka\u0161le a podobn\u011b, trv\u00e1 n\u011bkolik dn\u00ed a\u017e t\u00fddn\u016f a je nutn\u00e1 hospitalizace<\/li>\n<\/ul>\n<h2>Progn\u00f3za cystick\u00e9 fibr\u00f3zy<\/h2>\n<p>Progn\u00f3za onemocn\u011bn\u00ed je <strong>t\u00edm lep\u0161\u00ed, \u010d\u00edm d\u0159\u00edve se za\u010dne s l\u00e9\u010dbou<\/strong>. Proto je novorozeneck\u00fd screening na cystickou fibr\u00f3zu v\u00fdznamn\u00fdm miln\u00edkem v l\u00e9\u010db\u011b.<\/p>\n<p><strong>Pr\u016fm\u011brn\u00fd do\u017eit\u00fd v\u011bk<\/strong> pacient\u016f s cystickou fibr\u00f3zou byl v roce 2005 <strong>36,5 roku<\/strong>. V sou\u010dasnosti je toto \u010d\u00edslo o n\u011bco vy\u0161\u0161\u00ed a je p\u0159edpoklad, \u017ee se bude do budoucna vlivem pokroku medic\u00edny je\u0161t\u011b zvy\u0161ovat. N\u011bkter\u00e9 zdroje uv\u00e1d\u011bj\u00ed, \u017ee <strong>d\u00edt\u011b narozen\u00e9 v sou\u010dasnosti s cystickou fibr\u00f3zou se do\u017eije 40. roku \u017eivota<\/strong>.<\/p>\n<h2>Z\u00e1v\u011br<\/h2>\n<p>Cystick\u00e1 fibr\u00f3za je <strong>vrozen\u00e9 genetick\u00e9 onemocn\u011bn\u00ed<\/strong>.<\/p>\n<p>V sou\u010dasnosti je ve v\u011bt\u0161in\u011b p\u0159\u00edpad\u016f diagnostikov\u00e1na hned po narozen\u00ed d\u00edt\u011bte, kdy se d\u011bl\u00e1 takzvan\u00fd novorozeneck\u00fd screening. Typick\u00fdm p\u0159\u00edznakem, podle kter\u00e9ho pozn\u00e1te cystickou fibr\u00f3zu je <strong>slan\u00e1 poko\u017eka<\/strong>.<\/p>\n<p>I p\u0159es velk\u00fd pokrok v medic\u00edn\u011b pro n\u00e1s cystick\u00e1 fibr\u00f3za <strong>z\u016fst\u00e1v\u00e1 nel\u00e9\u010diteln\u00e9 onemocn\u011bn\u00ed<\/strong>. V sou\u010dasnosti dok\u00e1\u017eeme jen zkvalitnit a prodlou\u017eit \u017eivot pacienta. Pom\u00e1haj\u00ed n\u00e1m na to r\u016fzn\u00e9 <strong>l\u00e9ky odstra\u0148uj\u00edc\u00ed hlen a rehabilita\u010dn\u00ed techniky<\/strong>.<\/p>\n<div class='erit-toggle-block'>\n      <input type='checkbox' id='erit-toggle-block-checkbox-XkWITZ' class='erit-toggle-block-checkbox'\/>\n                  <label for='erit-toggle-block-checkbox-XkWITZ' class='erit-toggle-block-header'>Zdroje:<\/label>\n                  <div class='erit-toggle-block-content'>\n<ul>\n<li><a href=\"http:\/\/slanedeti.sk\/cms\/cysticka-fibroza-klinicke-prejavy-a-liecba\/910\" target=\"_blank\" rel=\"nofollow noopener noreferrer\">slanedeti.sk<\/a><\/li>\n<li><a href=\"https:\/\/www.medscape.com\/answers\/1001602-31223\/what-is-the-prognosis-of-cystic-fibrosis-cf\" target=\"_blank\" rel=\"nofollow noopener noreferrer\">medscape.com<\/a><\/li>\n<li><a href=\"http:\/\/www.solen.sk\/index.php?page=pdf_view&amp;pdf_id=2368\" target=\"_blank\" rel=\"nofollow noopener noreferrer\">solen.sk<\/a><\/li>\n<li><a href=\"https:\/\/www.mayoclinic.org\/diseases-conditions\/cystic-fibrosis\/symptoms-causes\/syc-20353700\" target=\"_blank\" rel=\"nofollow noopener noreferrer\">mayoclinic.org<\/a><\/li>\n<li><a href=\"https:\/\/www.cff.org\/What-is-CF\/About-Cystic-Fibrosis\/\" target=\"_blank\" rel=\"nofollow noopener noreferrer\">cff.org<\/a><\/li>\n<\/ul>\n<\/div>\n              <\/div>\n<div class='erit-disclaimer'><span class='erit-disclaimer-icon'><span class='erit-disclaimer-text'>!<\/span><\/span><span class='erit-disclaimer-text'>\u010cl\u00e1nek byl vypracov\u00e1n l\u00e9k\u00e1rn\u00edkem av\u0161ak, slou\u017e\u00ed pouze pro informativn\u00ed \u00fa\u010dely - nenahrazuje l\u00e9ka\u0159sk\u00e9 vy\u0161et\u0159en\u00ed, nebo osobn\u00ed setk\u00e1n\u00ed v l\u00e9k\u00e1rn\u011b.<\/span><\/div>\n<script type='text\/javascript' >\n                jQuery(document).ready(function($) {\n    \n                    let data = {\n                        'action': 'render_widget_action',\n                        'postId': null,\n                        'categoryId': null\n                    };\n    \n                    let ajaxUrlFromPHP = 'https:\/\/zdravovek.eu\/wp-admin\/admin-ajax.php';\n                    jQuery.post(ajaxUrlFromPHP, data, function(response) {\n                        if(response == 0){\n                            \/\/ chyba\n                            jQuery( '#eap_top_w' ).html( '' );\n                            jQuery( '#eap_top_w_wrap' ).hide();\n                        } if(response == -1){\n                            \/\/ nenasli ziadne produkty\n                            jQuery( '#eap_top_w' ).html( '' );\n                            jQuery( '#eap_top_w_wrap' ).hide();\n                        } else {\n                            let desktop = $(window).width() > 960;\n                            if(desktop){\n                                jQuery( '#eap_top_w' ).html( response );\n                                jQuery( '#eap_top_w_wrap' ).fadeIn(1000);\n                            } else {\n                                jQuery( '#eap_top_w_mob_chart' ).html( response );\n                                jQuery( '#eap_top_w_mob' ).fadeIn(1000); 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Postihuje zejm\u00e9na pl\u00edce, ale i jin\u00e9 org\u00e1ny. Jedn\u00edm z nejzn\u00e1m\u011bj\u0161\u00edch p\u0159\u00edznak\u016f cystick\u00e9 fibr\u00f3zy je slan\u00e1 poko\u017eka d\u00edt\u011bte. Proto se n\u011bkdy ozna\u010duje tak\u00e9 jako nemoc slan\u00fdch d\u011bt\u00ed. P\u0159e\u010dt\u011bte si, jak cystick\u00e1 fibr\u00f3za vznik\u00e1, jak\u00e9 jsou jej\u00ed nej\u010dast\u011bj\u0161\u00ed projevy a jak\u00e1 je progn\u00f3za p\u0159i l\u00e9\u010db\u011b t\u00e9to n\u00e1ro\u010dn\u00e9 choroby. Co to [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":17908,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":[],"categories":[34,79],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v15.8 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cystick\u00e1 fibr\u00f3za - projevy, diagnostika, progn\u00f3za | Zdravov\u011bk<\/title>\n<meta name=\"description\" content=\"Co je to cystick\u00e1 fibr\u00f3za? Jak\u00e9 m\u00e1 projevy? 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